Inherited Arrhythmias in Children
نویسنده
چکیده
Sinus node dysfunction has been described as an inherited (autosomal recessive form) problem by Benson et al1. The cause seems to be certain specific mutations on the SCN5A gene. Patients with long QT type 3 (SCN5A mutation) have sinus bradycardia as part of the spectrum of abnormalities in this disease2. Atrial standstill is a rare condition where the atrium is silent i.e. there is no electrical activity present and also the atrium is not excitable by pacing. Rare, inherited forms of this condition have been described3,4.
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